| Title： | Chinese expert consensus on the hyper-IgE syndrome |
| Edition： | Original |
| Classification： | Experts consensus |
| Field： | Diagnosis and Treatment |
| Countries and regions： | China |
| Guidelines users： | Clinician |
| Evidence classification method： | NO |
| Development unit： | China Medicine Education Association Committee on Pediatrics |
| Registration time: | 2024-01-03 |
| Registration number： | PREPARE-2024CN120 |
| Purpose of the guideline: | The hyper-IgE syndromes (HIES) is a group of rare primary immunodeficiency diseases with significantly elevated serum IgE, eczema and recurrent infections as the triad. It was first recognized in 1966 when Davis first reported "Job Syndrome". In recent years, advances in genetic testing have enabled the identification of more HIES types. However, the early diagnosis of HIES remains a challenge, as it is difficult to distinguish HIES from other diseases characterized by eczema and high IgE early in life, therefore, this expert consensus was developed for clinicians to better identify early and standardize the treatment of HIES. |
CURRENT Guidelines INFORMATION
Uploader：Zhongguoyiyaojiaoyuxiehuierkezhuanweihui
Upload Date：2024-01-03
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